TY - JOUR T1 - REPORT OF FOUR CASES OF FAMILIAL IDIOPATHIC PULMONARY FIBROSIS TT - JF - MJIRI JO - MJIRI VL - 2 IS - 4 UR - http://mjiri.iums.ac.ir/article-1-1241-en.html Y1 - 1989 SP - 313 EP - 316 N2 - A 25 year old male and his 46 year old aunt presented with shortness of breath and a dramatic response to steroids. The other two patients are sisters with more advanced disease. One of these responded partially to steroids, while the other died within 4 months of treatment. The genetic basis and pathogenesis are discussed. M3 ER -