en Urology and Nephrology Urology and Nephrology case report case report <p>  Distal renal tubular acidosis is a syndrome of abnormal urine acidification and is characterized by hyperchloremic metabolic acidosis, hypokalemia, hypercalciurea, nephrocalcinosis and nephrolithiasis. Despite the presence of persistent hypokalemia, acute muscular paralysis is rarely encountered in males.Here, we will report an eighteen year old male patient who presented with flaccid quadriparesis and was subsequently found to have rhabdomyolysis, severe short stature, skeletal deformities and primary distal renal tubular acidosis. </p> Nephrocalcinosis, Hypokalemia, Rhabdomyolysis, Short stature, Renal tubular acidosis. 221 225 http://mjiri.iums.ac.ir/browse.php?a_code=A-10-1-664&slc_lang=en&sid=1 Manzoor Ahmad Bhat manzoor93@gmail.com 200319475328460012881 200319475328460012881 Yes Department of Endocrinology, Sher-I-Kashmir Instituite of Medical Sciences, Soura Srinagar Jammu and Kashmir India. Bashir Ahmad Laway drlaway@gmail.com 200319475328460012882 200319475328460012882 No 2. Department of Endocrinology, Sher-I-Kashmir Instituite of Medical Sciences, Soura Srinagar Jammu and Kashmir India. Farhat Mustafa mustafafarhat4@gmail.com 200319475328460012883 200319475328460012883 No 3. Department of Internal, government medical college, Srinagar Jammu and Kashmir India. Mohammad Shafi Kuchay drshafikuchay@gmail.com 200319475328460012884 200319475328460012884 No . Department of Endocrinology, Sher-I-Kashmir Instituite of Medical Sciences, Soura Srinagar Jammu and Kashmir India. Idrees Mubarik munn3147@yahoo.com 200319475328460012885 200319475328460012885 No Department of Endocrinology, Sher-I-Kashmir Instituite of Medical Sciences, Soura Srinagar Jammu and Kashmir India. Nazir Ahmad Palla manzoor93@hotmail.com 200319475328460012886 200319475328460012886 No Department of Endocrinology, Sher-I-Kashmir Instituite of Medical Sciences, Soura Srinagar Jammu and Kashmir India.