en Radiology Radiology case report case report Macrodystrophia lipomatosa is a rare congenital form of localized gigantism characterized by an increase in all mesenchymal elements, particularly fibroadipose tissue. MR imaging can be used to examine the soft tissue and detect the fibrous and fatty hypertrophy that characterizes this condition and also diagnose an associated fibrolipomatous hamartoma of the median or plantar nerve. We describe the clinical and radiological findings (including CT scan, MRI and bone scan) and also progression of this rare entity during a 10 year period. Macrodystrophia lipomatosa (MDL), Fibrolipomatous hamartoma (FLH). Magnetic resonance imaging, Computed tomography 111 114 http://mjiri.iums.ac.ir/browse.php?a_code=A-10-298-219&slc_lang=en&sid=1 MARYAM RAHMANI 20031947532846004017 20031947532846004017 Yes From the Department of Radiology, Emam Khomeini Medical Center; Tehran University of Medical Sciences, Tehran, I.R. Iran. MOHAMMAD ALI SHABANI 20031947532846004018 20031947532846004018 No