TALEI A R, MALEKHOSSEINI S A, ATTARAN S Y, OWJI S M, KUMAR P V. IMM UNOPROLIFER ATI VE SMALL INTES TINAL DISEASE (ALPHA HEAVY CHAIN DISEASE) : UNUSU AL PRESENTATION WI TH ABDOMINAL MASS. Med J Islam Repub Iran 1997; 11 (3) :263-266
URL:
http://mjiri.iums.ac.ir/article-1-1105-en.html
From the Departments of Surgery and Pathology, Shiraz University of Medical Sciences, Shiraz, Islamic Republic of Iran
Abstract: (5157 Views)
During the period of 1984-1995, nine young patients were admitted to Shiraz
University Hospitals with a chief complaint of abdominal mass, weight loss and
chronic diarrhea. Clinically, these cases were diagnosed as intestinal tuberculosis
or lymphoma. Laparotomy revealed a huge mass involving the upper small
intestine. Histologic sections showed diffuse infiltration of the intestinal wall with
numerous mature and immature plasma cells. Serological tests showed increased
levels of IgA. These cases were diagnosed and treated as immunoproliferative
small intestinal disease (IPSID). Follow-up of these patients revealed that seven
patients died 6-8 months after the operation and the other two patients were lost
to follow-up.
Type of Study:
case report |
Subject:
Surgery