From the Department of Pediatrics, Shahid Rajai Heart Hospital, Iran University of Medical Sciences,
Abstract: (4045 Views)
During 15 years from 1975 to 1990, thirteen cases of supravalvar aortic
stenosis were admitted at the pediatrics department of Shahid Rajai Heart
Hospital, Tehran. All patients were subjected to cardiac catheterization and a
angiocardiography. Patients ranged in age from 3.5 years to 14 years with a
mean of 8.7 years.
Seventy seven percent of childen were male. Eight cases (61.5%) had
Williams' syndrome. Hourglass type of supravalvar aortic stenosis was the
most common variant (70%), followed by hypoplastic type (15%) and
membranous type (5%). Peripheral pulmonary stenosis was the most common
associated anomaly and was observed in 23% of patients.
The main purpose of this investigation is to report the results of the study
on supravalvar aortic stenosis and its association with Williams' syndrome in a
group of Iranian children.
Type of Study:
Original Research |
Subject:
Pediatric