Medical Journal of The Islamic Republic of Iran (MJIRI)

 Abstract

 Liver neoplasm is not an uncommon disease in Asian countries. Liposarcoma is a rare mesenchymal malignant tumor which usually originates in the retroperitoneum and extremities. From 1973 till now about 10 cases of primary liver liposarcoma have been reported. We present the eleventh case in a young adult female with uncommon presentation. She suffered from a huge mass in the right portion of the liver with clinical manifestations of sepsis and respiratory distress. Despite aggressive surgery, tumor recurrence after six months led to death after a year. Hepatectomy is the best strategy to achieve long term survival for patients.Trials of preoperative radiation therapy with or without intraoperative irradiation are underway.