From the Ophthalmology Department, Shahid Labbafi Nejad Medical Center, Shahid Beheshli University of Medical Sciences, Tehran, Islamic Republic of Iran.
Abstract: (4771 Views)
Anterior megalophthalmos is a developmental anomaly of the anterior
ocular segment. This is an X-linked recessive disease and manifests as
bilateral enlarged corneas, open iridocorneal angle, hypoplastic iris and
dislocation and opacification of an apparently small lens.
We have also observed obvious vitreoretinal degeneration in our patients.
What may threaten visual acuity later is an open angle glaucoma and
retinal detachment. It should be distinguished from simple megalocornea
and congenital glaucomatous buphthalmos. Two cases of anterior megalophthalmos
in one family are presented and discussed here.